Personal tools Not logged in Talk Contributions Log in. Thank you for your comments. Thank you for reviewing this article. Your review hasn't been inserted one review per article per day allowed! You might also have this test if your healthcare provider suspects that you have a rare urea cycle disorder or Reye syndrome. Reye syndrome is a potentially fatal disease that affects the brain and liver.
Children may have this test if they frequently vomit or are very tired within a week after a virus-related illness. If your healthcare provider suspects that you have a urea cycle disorder, he or she may order other tests that look at ammonia levels in your body. Many things may affect your lab test results. These include the method each lab uses to do the test.
Even if your test results are different from the normal value, you may not have a problem. To learn what the results mean for you, talk with your healthcare provider.
People who have a portacaval shunt in their liver to treat high blood pressure may also have higher levels of ammonia. Levels that are lower than normal can mean that your kidneys aren't removing waste as they should. The test requires a blood sample, which is drawn through a needle from a vein in your arm.
Philadelphia, PA: Elsevier; chap Inborn errors of metabolism. Fanaroff and Martin's Neonatal-Perinatal Medicine. Inborn errors of urea synthesis. Swaiman's Pediatric Neurology: Principles and Practice. Updated by: Anna C. Review provided by VeriMed Healthcare Network. Editorial team. Hereditary urea cycle abnormality. Symptoms include: Confusion Decreased food intake Dislike of foods that contain protein Increased sleepiness, difficulty waking up Nausea, vomiting.
Exams and Tests. The health care provider will often diagnose these disorders when the child is still an infant.
Signs may include: Abnormal amino acids in blood and urine Abnormal level of orotic acid in blood or urine High blood ammonia level Normal level of acid in blood Tests may include: Arterial blood gas Blood ammonia Blood glucose Plasma amino acids Urine organic acids Genetic tests Liver biopsy MRI or CT scan. It is very important for people with these disorders to avoid fasting.
Outlook Prognosis. How well people do depends on: Which urea cycle abnormality they have How severe it is How early it is discovered How closely they follow a protein-restricted diet Babies diagnosed in the first week of life and put on a protein-restricted diet right away may do well. Possible Complications. Abstract Free ammonium ions are produced and consumed during cell metabolism.
Publication types Review. Substances Quaternary Ammonium Compounds.
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